Rare Clinical Case: Solid Pseudopapillary tumor of pancreas.

Authors

  • S. I. Karpenko
  • I. S. Shponka
  • V. F. Zavizion
  • E. M. Zavizion
  • V. R. Skoryk
  • A. V. Snisar

DOI:

https://doi.org/10.26641/2307-0404.2016.1.64269

Keywords:

solid pseudopapillary tumor of pancreas, diagnostics, clinical observation

Abstract

Solid pseudopapillary tumor of the pancreas (Frantz's tumor) is a very rare disease with uncertain malignant potential. This tumor occurs in young women at the age before 35 years. Asymptomatic disease course leads to growth of tumor up to the huge size. Surgery is the only treatment method applied. Histological diagnostic is complicated with similarity of tumor with neuroendocrine tumor of the pancreas. Disease is characterized with favorable prognosis. Paper shows our own clinical observation of Frantz’s tumor. During control ultrasound examination of woman aged 34 years, echo-signs of mass lesion in extraperitoneal area near the lower pole of the left kidney were diagnosed. During physical examination in the left hypochondrium a soft, atropic mass lesion 5.5x5 cm in size was diagnosed. Lesion presence is confirmed by CT assessment. Distal resection of the pancreas and splenectomy was performed. Diagnosis was verified histologically and immunohistochemically. Postoperative period is complications free. The results of CT assessment, detailed description of gross specimen and the results of histological and immunohistochemical examination are presented.

Author Biographies

S. I. Karpenko

SE «Dnipropetrovsk medical academy of Health Ministry of Ukraine»
Department of surgery N 2

I. S. Shponka

Department of pathological anatomy and forensic medicine

V. F. Zavizion

Department of Oncology and medical radiology

E. M. Zavizion

SE «Dnipropetrovsk medical academy of Health Ministry of Ukraine»
Department of surgery N 2

V. R. Skoryk

Department of pathological anatomy and forensic medicine

A. V. Snisar

Dzerzhinsky str., 9, Dnipropetrovsk, 49044, Ukraine
Dnipropetrovsk regional clinical hospital named after. I. I. Mechnikov Dnipropetrovsk, 49044, Ukraine

References

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Published

2016-03-09

How to Cite

1.
Karpenko SI, Shponka IS, Zavizion VF, Zavizion EM, Skoryk VR, Snisar AV. Rare Clinical Case: Solid Pseudopapillary tumor of pancreas. Med. perspekt. [Internet]. 2016Mar.9 [cited 2024Apr.27];21(1):144-8. Available from: https://journals.uran.ua/index.php/2307-0404/article/view/64269

Issue

Vol. 21 No. 1 (2016)

Section

A CASE FROM PRACTICE

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